Hemorrhagic fever - renal syndrome
General Information (adopted from Orphanet):
Synonyms, Signs: |
Hantavirus fever Hantavirosis |
Number of Symptoms | 33 |
OrphanetNr: | 340 |
OMIM Id: |
|
ICD-10: |
A98.5 |
UMLs: |
C0019101 C2930957 |
MeSH: |
C535630 D006480 |
MedDRA: |
10023484 |
Snomed: |
102455002 364756009 |
Prevalence, inheritance and age of onset:
Prevalence: | No data available. |
Inheritance: |
|
Age of onset: |
|
Disease classification (adopted from Orphanet):
Parent Diseases: |
Viral hemorrhagic fever
-Rare infectious disease |
Symptom Information:
|
(HPO:0001970) | Tubulointerstitial nephritis | Frequent [Orphanet] | 27 / 7739 | |||
|
(HPO:0000083) | Renal insufficiency | Frequent [Orphanet] | 232 / 7739 | |||
|
(HPO:0011037) | Decreased urine output | Frequent [Orphanet] | 47 / 7739 | |||
|
(HPO:0000093) | Proteinuria | Frequent [Orphanet] | 169 / 7739 | |||
|
(HPO:0000124) | Renal tubular dysfunction | Frequent [Orphanet] | 46 / 7739 | |||
|
(HPO:0100576) | Amaurosis fugax | Occasional [Orphanet] | 13 / 7739 | |||
|
(HPO:0100533) | Inflammatory abnormality of the eye | Frequent [Orphanet] | 70 / 7739 | |||
|
(HPO:0000613) | Photophobia | Frequent [Orphanet] | 158 / 7739 | |||
|
(HPO:0000545) | Myopia | Occasional [Orphanet] | 286 / 7739 | |||
|
(HPO:0012375) | Chemosis | Frequent [Orphanet] | 7 / 7739 | |||
|
(HPO:0002315) | Headache | Frequent [Orphanet] | 175 / 7739 | |||
|
(HPO:0005059) | Arthralgia/arthritis | Frequent [Orphanet] | 141 / 7739 | |||
|
(HPO:0002239) | Gastrointestinal hemorrhage | Occasional [Orphanet] | 97 / 7739 | |||
|
(HPO:0002910) | Elevated hepatic transaminases | Frequent [Orphanet] | 158 / 7739 | |||
|
(HPO:0002027) | Abdominal pain | Frequent [Orphanet] | 184 / 7739 | |||
|
(HPO:0000822) | Hypertension | Occasional [Orphanet] | 224 / 7739 | |||
|
(HPO:0002615) | Hypotension | Occasional [Orphanet] | 52 / 7739 | |||
|
(HPO:0011675) | Arrhythmia | Occasional [Orphanet] | 226 / 7739 | |||
|
(HPO:0001697) | Abnormality of the pericardium | Occasional [Orphanet] | 52 / 7739 | |||
|
(HPO:0001637) | Abnormality of the myocardium | Occasional [Orphanet] | 76 / 7739 | |||
|
(HPO:0002170) | Intracranial hemorrhage | Occasional [Orphanet] | 40 / 7739 | |||
|
(HPO:0001873) | Thrombocytopenia | Frequent [Orphanet] | 224 / 7739 | |||
|
(HPO:0001974) | Leukocytosis | Frequent [Orphanet] | 33 / 7739 | |||
|
(HPO:0003075) | Hypoproteinemia | Frequent [Orphanet] | 27 / 7739 | |||
|
(HPO:0001945) | Fever | Very frequent [Orphanet] | 218 / 7739 | |||
|
(HPO:0002093) | Respiratory insufficiency | Frequent [Orphanet] | 410 / 7739 | |||
|
(HPO:0002113) | Pulmonary infiltrates | Frequent [Orphanet] | 36 / 7739 | |||
|
(HPO:0100750) | Atelectasis | Frequent [Orphanet] | 17 / 7739 | |||
|
(HPO:0002103) | Abnormality of the pleura | Frequent [Orphanet] | 58 / 7739 | |||
|
(HPO:0002105) | Hemoptysis | Occasional [Orphanet] | 30 / 7739 | |||
|
(HPO:0003326) | Myalgia | Frequent [Orphanet] | 143 / 7739 | |||
|
(HPO:0001324) | Muscle weakness | Very frequent [Orphanet] | 859 / 7739 | |||
|
(HPO:0001522) | Death in infancy | Occasional [Orphanet] | 275 / 7739 |
Associated genes:
ClinVar (via SNiPA)
Gene symbol | Variation | Clinical significance | Reference |
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