Pulmonary sequestration

Symptom Information:

Symptom ID: HPO:0100632
Synonyms:
Bronchopulmonary sequestration [HPO:0100632]
Cystic lung lesion [HPO:0100632]
Congenital sequestration of lung (disorder) [Orphanet:32400]
Bronchopulmonary Sequestration [Orphanet:32400]
Absent lobe/lung/segmentation defect/abnormal lobulation/sequestration [Orphanet:32400]
Pulmonary sequestration [Orphanet:32400]
Pulmonary sequestration [MedDRA:10059160]
Lung lobe congenital absence [Orphanet:32400]
Quality:
Cross references:
HPO:0010962 "Extralobar sequestration" [Orphanet:32400]
Orphanet:32400 "Absent lobe/lung/segmentation defect/abnormal lobulation/sequestration" [Orphanet:32400]
UMLS:C0006288 "Bronchopulmonary Sequestration" [Orphanet:32400]
Is a (Direct Parents):
HPO         Abnormal lung lobation
MedDRA Pulmonary and bronchial disorders congenital
Orphanet Abnormality of the diaphragm
Orphanet Abnormal lung lobation
Is a (Whole tree): HPO:
All(HPO:0000001)
    Phenotypic abnormality(HPO:0000118)
       Abnormality of the respiratory system(HPO:0002086)
          Abnormal respiratory system morphology(HPO:0012252)
             Abnormality of lung morphology(HPO:0002088)
                Abnormal lung lobation(HPO:0002101)
                   Pulmonary sequestration(HPO:0100632)
MedDRA:
Congenital, familial and genetic disorders(MedDRA:10010331)
    Respiratory disorders congenital(MedDRA:10038686)
       Pulmonary and bronchial disorders congenital(MedDRA:10025039)
          Pulmonary sequestration(HPO:0100632)
Database Frequency: 0 / 7739
Resource:

All diseases associated with this symptom: