Magy et al. (1997) described a French family in which 8 living members and 4 deceased members in 4 generations, in an autosomal dominant pedigree pattern, had a hereditary neuropathy with probable thermosensitivity. Patients presented with reversible episodes ... Magy et al. (1997) described a French family in which 8 living members and 4 deceased members in 4 generations, in an autosomal dominant pedigree pattern, had a hereditary neuropathy with probable thermosensitivity. Patients presented with reversible episodes of ascending muscle weakness, paresthesias, and areflexia apparently triggered by an elevation of body temperature over 38.5 degrees C. Mean age at onset was 13 +/- 12 years (SD; range, 6 to 43). Four patients had suffered up to 5 attacks. EMG and pathologic findings were compatible with a reversible demyelinating neuropathy such as Guillain-Barre syndrome (139393).