Lichen planopilaris

General Information (adopted from Orphanet):

Synonyms, Signs: LPP
Lichen follicularis
Follicular lichen planus
Lichen planus follicularis
Number of Symptoms 17
OrphanetNr: 525
OMIM Id:
ICD-10: L66.1
UMLs: C0023645
MeSH: C535892
MedDRA:
Snomed: 64540004

Prevalence, inheritance and age of onset:

Prevalence: No data available.
Inheritance: Not applicable
[Orphanet]
Age of onset: Adult
[Orphanet]

Disease classification (adopted from Orphanet):

Parent Diseases: Alopecia
 -Rare genetic disease
 -Rare skin disease
Rare cutaneous lichen planus
 -Rare skin disease

Symptom Information: Sort by abundance 

1
 (HPO:0100650) Vaginal neoplasm Occasional [Orphanet] 6 / 7739
2
 (HPO:0100649) Neoplasm of the oral cavity Occasional [Orphanet] 20 / 7739
3
 (HPO:0001059) Pterygium Occasional [Orphanet] 16 / 7739
4
 (HPO:0001396) Cholestasis Occasional [Orphanet] 136 / 7739
5
 (HPO:0002250) Abnormality of the large intestine Occasional [Orphanet] 32 / 7739
6
 (HPO:0200042) Skin ulcer Frequent [Orphanet] 138 / 7739
7
 (HPO:0008065) Aplasia/Hypoplasia of the skin Frequent [Orphanet] 81 / 7739
8
 (HPO:0001806) Onycholysis Occasional [Orphanet] 20 / 7739
9
 (HPO:0001053) Hypopigmented skin patches Occasional [Orphanet] 80 / 7739
10
 (HPO:0010783) Erythema Very frequent [Orphanet] 138 / 7739
11
 (HPO:0100725) Lichenification Very frequent [Orphanet] 14 / 7739
12
 (HPO:0001231) Abnormality of the fingernails Frequent [Orphanet] 116 / 7739
13
 (HPO:0001596) Alopecia Very frequent [Orphanet] 162 / 7739
14
 (HPO:0000962) Hyperkeratosis Very frequent [Orphanet] 216 / 7739
15
 (HPO:0200037) Skin vesicle Occasional [Orphanet] 102 / 7739
16
 (HPO:0000989) Pruritus Frequent [Orphanet] 111 / 7739
17
 (HPO:0030350) Erythematous papule Very frequent [Orphanet] 123 / 7739

Associated genes:

ClinVar (via SNiPA)

Gene symbol Variation Clinical significance Reference

Additional Information: