|
1
|
(HPO:0004890)
|
Elevated pulmonary artery pressure |
Very frequent [IBIS]
|
100% (n=11)
|
11115457
|
IBIS
|
8 / 7739
|
|
2
|
(HPO:0002094)
|
Dyspnea |
Very frequent [IBIS]
|
100% (n=11)
|
11115457
|
IBIS
|
132 / 7739
|
|
3
|
(HPO:0002113)
|
Pulmonary infiltrates |
Very Frequent [IBIS]
|
91% (n=11)
|
11115457
|
IBIS
|
36 / 7739
|
|
4
|
(MedDRA:10065906)
|
Carbon monoxide diffusing capacity decreased |
Frequent [IBIS]
|
81% (n=11)
|
19634080
|
IBIS
|
8 / 7739
|
|
5
|
(MedDRA:10019024)
|
Haemosiderosis |
Frequent [IBIS]
|
64% (n=9)
|
11115457
|
IBIS
|
1 / 7739
|
|
6
|
(MedDRA:10047240)
|
Venous pressure jugular increased |
Frequent [IBIS]
|
64% (n=11)
|
11115457
|
IBIS
|
6 / 7739
|
|
7
|
(HPO:0012735)
|
Cough |
Frequent [IBIS]
|
55% (n=11)
|
11115457
|
IBIS
|
24 / 7739
|
|
8
|
(HPO:0002202)
|
Pleural effusion |
Frequent [IBIS]
|
36% (n=11)
|
11115457
|
IBIS
|
22 / 7739
|
|
9
|
(HPO:0002716)
|
Lymphadenopathy |
Frequent [IBIS]
|
33% (n=9)
|
11115457
|
IBIS
|
129 / 7739
|
|
10
|
(HPO:0000961)
|
Cyanosis |
Occasionally [IBIS]
|
27% (n=11)
|
11115457
|
IBIS
|
60 / 7739
|
|
11
|
(HPO:0001698)
|
Pericardial effusion |
Occasionally [IBIS]
|
22% (n=9)
|
11115457
|
IBIS
|
20 / 7739
|
|
12
|
(HPO:0100749)
|
Chest pain |
Occasionally [IBIS]
|
18% (n=11)
|
11115457
|
IBIS
|
92 / 7739
|
|
13
|
(HPO:0002092)
|
Pulmonary hypertension |
|
|
19634080
|
IBIS
|
109 / 7739
|
|
14
|
(OMIM)
|
Prominent second heart sound |
|
|
23235992
|
IBIS
|
1 / 7739
|
|
15
|
(OMIM)
|
Centrilobular ground glass opacities seen on CT |
|
|
19634080
|
IBIS
|
3 / 7739
|
|
16
|
(OMIM)
|
Thickened interlobular septae seen on CT |
|
|
9440597
|
IBIS
|
2 / 7739
|
|
17
|
(OMIM)
|
Occult alveolar hemorrhage |
|
|
19634080
|
IBIS
|
1 / 7739
|
|
18
|
(HPO:0001708)
|
Right ventricular failure |
|
|
19634080
|
IBIS
|
11 / 7739
|
|
19
|
(HPO:0011718)
|
Abnormality of the pulmonary veins |
|
|
19634080; 24853728
|
IBIS
|
6 / 7739
|
|
20
|
(HPO:0100598)
|
Pulmonary edema |
|
|
24548200
|
IBIS
|
17 / 7739
|
|
21
|
(MedDRA:10037313)
|
Pulmonary alveolar haemorrhage |
|
|
19634080
|
IBIS
|
2 / 7739
|
|
22
|
(OMIM)
|
[DEL] Thickened alveolar septa |
|
|
19634080
|
IBIS
|
3 / 7739
|
|
23
|
(HPO:0012415)
|
Abnormal blood gas level |
|
|
19634080
|
IBIS
|
9 / 7739
|
|
24
|
(MedDRA:10037396)
|
Pulmonary haemosiderosis |
|
|
24548200
|
IBIS
|
1 / 7739
|
|
25
|
(MedDRA:10025080)
|
Lung consolidation |
|
|
23886653
|
IBIS
|
5 / 7739
|
|
26
|
(MedDRA:10060237)
|
Right ventricular systolic pressure decreased |
|
|
23886653
|
IBIS
|
1 / 7739
|
|
27
|
(HPO:0005312)
|
Pulmonary aterial intimal fibrosis |
|
|
23886653
|
IBIS
|
3 / 7739
|
|
28
|
(HPO:0001279)
|
Syncope |
|
|
23886653
|
IBIS
|
94 / 7739
|
|
29
|
(HPO:0100721)
|
Mediastinal lymphadenopathy |
|
|
23886653
|
IBIS
|
19 / 7739
|
|
30
|
(HPO:0012418)
|
Hypoxemia |
|
|
18626305
|
IBIS
|
18 / 7739
|
|
31
|
(HPO:0001640)
|
Cardiomegaly |
|
|
9440597
|
IBIS
|
81 / 7739
|
|
32
|
(MedDRA:10033318)
|
Oxygen saturation decreased |
|
|
9440597
|
IBIS
|
4 / 7739
|
|
33
|
(HPO:0001667)
|
Right ventricular hypertrophy |
|
|
9440597
|
IBIS
|
23 / 7739
|
|
34
|
(HPO:0001707)
|
Abnormality of the right ventricle |
|
|
9440597
|
IBIS
|
7 / 7739
|
|
35
|
(HPO:0005180)
|
Tricuspid regurgitation |
|
|
9440597
|
IBIS
|
20 / 7739
|
|
36
|
(MedDRA:10062049)
|
Lymphocytic infiltration |
|
|
11069841
|
IBIS
|
9 / 7739
|
|
37
|
(HPO:0001217)
|
Clubbing |
|
|
11115457
|
IBIS
|
39 / 7739
|
|
38
|
(HPO:0006518)
|
Pulmonary venous occlusion |
|
|
9440597
|
IBIS
|
2 / 7739
|
|
39
|
(HPO:0002093)
|
Respiratory insufficiency |
|
|
18626305
|
IBIS
|
410 / 7739
|
|
40
|
(OMIM)
|
Reduced diffusion capacity |
|
|
9645575
|
IBIS
|
8 / 7739
|
|
41
|
(HPO:0002088)
|
Abnormality of lung morphology |
|
|
19634080
|
IBIS
|
11 / 7739
|