Congenital disorder of glycosylation with dilated cardiomyopathy
General Information (adopted from Orphanet):
Synonyms, Signs: |
CDG with dilated cardiomyopathy |
Number of Symptoms | 0 |
OrphanetNr: | 371176 |
OMIM Id: |
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ICD-10: |
E77.8 |
UMLs: |
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MeSH: |
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MedDRA: |
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Snomed: |
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Prevalence, inheritance and age of onset:
Prevalence: | No data available. |
Inheritance: |
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Age of onset: |
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Disease classification (adopted from Orphanet):
Parent Diseases: |
Familial dilated cardiomyopathy
-Rare cardiac disease -Rare genetic disease |
Comment:
This term does not characterize a disease but a group of diseases. Annotations can be found at a more specific level. |
Symptom Information:
Associated genes:
ClinVar (via SNiPA)
Gene symbol | Variation | Clinical significance | Reference |
---|---|---|---|
DOLK | rs137853109 | pathogenic | RCV000001190.2 |
DOLK | rs137853110 | pathogenic | RCV000001191.2 |
DOLK | rs387907030 | pathogenic | RCV000023835.2 |
DOLK | rs587777137 | pathogenic | RCV000087064.3 |
PGM1 | rs121918371 | pathogenic | RCV000014620.27 |
PGM1 | rs397515423 | pathogenic | RCV000032991.26 |
PGM1 | rs398122912 | pathogenic | RCV000032990.25 |
PGM1 | rs587776801 | pathogenic | RCV000014621.28 |
PGM1 | rs587777401 | pathogenic | RCV000119799.3 |
PGM1 | rs587777402 | pathogenic | RCV000119800.3 |
PGM1 | rs587777403 | pathogenic | RCV000119801.3 |
PGM1 | rs587777404 | pathogenic | RCV000119802.3 |
PGM1 | rs587777405 | pathogenic | RCV000119803.3 |