Idiopathic intracranial hypertension

General Information (adopted from Orphanet):

Synonyms, Signs: IIH
pseudotumor cerebri
Benign intracranial hypertension
Number of Symptoms 6
OrphanetNr: 238624
OMIM Id: 243200
ICD-10: G93.2
UMLs:
MeSH:
MedDRA:
Snomed:

Prevalence, inheritance and age of onset:

Prevalence: No data available.
Inheritance: Autosomal recessive inheritance
[Omim]
Age of onset:

Disease classification (adopted from Orphanet):

Parent Diseases: Rare neurologic disease
 -Rare neurologic disease

Symptom Information: Sort by abundance 

1
(HPO:0001085) Papilledema 31 / 7739
2
(HPO:0002516) Increased intracranial pressure 47 / 7739
3
(HPO:0000822) Hypertension 224 / 7739
4
(OMIM) Idiopathic intracranial hypertension 1 / 7739
5
(HPO:0000007) Autosomal recessive inheritance 2538 / 7739
6
(OMIM) Pseudotumor cerebri 3 / 7739

Associated genes:

ClinVar (via SNiPA)

Gene symbol Variation Clinical significance Reference

Additional Information: