Familial restrictive cardiomyopathy
General Information (adopted from Orphanet):
Synonyms, Signs: |
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Number of Symptoms | 0 |
OrphanetNr: | 217635 |
OMIM Id: |
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ICD-10: |
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UMLs: |
C0340429 |
MeSH: |
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MedDRA: |
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Snomed: |
233878008 |
Prevalence, inheritance and age of onset:
Prevalence: | No data available. |
Inheritance: |
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Age of onset: |
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Disease classification (adopted from Orphanet):
Parent Diseases: |
Rare genetic cardiac disease
-Rare genetic disease Restrictive cardiomyopathy -Rare cardiac disease |
Comment:
This term does not characterize a disease but a group of diseases. Annotations can be found at a more specific level. |
Symptom Information:
Associated genes:
ClinVar (via SNiPA)
Gene symbol | Variation | Clinical significance | Reference |
---|---|---|---|
MT-RNR1 | rs267606617 | pathogenic | RCV000010256.5 |
MYH7 | rs397516142 | likely pathogenic | RCV000157359.1 |
MYH7 | rs397516153 | pathogenic | RCV000035799.3 |
MYH7 | rs727503260 | likely pathogenic | RCV000151276.1 |
MYH7 | rs730880154 | likely pathogenic | RCV000157347.1 |
MYPN | rs140148105 | pathogenic | RCV000043546.2 |
MYPN | rs199476408 | pathogenic | RCV000043547.2 |
MYPN | rs71534278 | pathogenic | RCV000043541.2 |
MYPN | rs71534280 | pathogenic | RCV000043543.2 |
MYPN | rs71584501 | pathogenic | RCV000043540.2 |
TNNI3 | rs104894724 | pathogenic | RCV000013239.22 |
TNNI3 | rs104894728 | pathogenic | RCV000013236.22 |
TNNI3 | rs104894729 | pathogenic | RCV000013237.22 |
TNNI3 | rs104894730 | pathogenic | RCV000013238.23 |
TNNI3 | rs121917760 | pathogenic | RCV000013241.22 |
TNNI3 | rs121917761 | pathogenic | RCV000013242.16 |
TNNI3 | rs727503504 | likely pathogenic | RCV000157530.1 |
TNNI3 | rs730880231 | pathogenic | RCV000157531.1 |
TNNT2 | rs121964855 | pathogenic | RCV000013219.23 |
TNNT2 | rs727503513 | likely pathogenic | RCV000152104.1 |