Mitochondrial disease with dilated cardiomyopathy
General Information (adopted from Orphanet):
Synonyms, Signs: |
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Number of Symptoms | 0 |
OrphanetNr: | 217613 |
OMIM Id: |
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ICD-10: |
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UMLs: |
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MeSH: |
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MedDRA: |
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Snomed: |
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Prevalence, inheritance and age of onset:
Prevalence: | No data available. |
Inheritance: |
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Age of onset: |
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Disease classification (adopted from Orphanet):
Parent Diseases: |
Familial dilated cardiomyopathy
-Rare cardiac disease -Rare genetic disease |
Comment:
This term does not characterize a disease but a group of diseases. Annotations can be found at a more specific level. |
Symptom Information:
Associated genes:
ClinVar (via SNiPA)
Gene symbol | Variation | Clinical significance | Reference |
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TAZ | rs104894937 | pathogenic | RCV000011857.5 |
TAZ | rs104894941 | pathogenic | RCV000011850.15 |
TAZ | rs104894942 | pathogenic | RCV000011859.5 |
TAZ | rs132630277 | pathogenic | RCV000011854.13 |
TAZ | rs387907218 | pathogenic | RCV000035099.2 |
TAZ | rs387907218 | pathogenic | RCV000029171.12 |
TAZ | rs397515738 | likely pathogenic | RCV000035087.2 |
TAZ | rs397515739 | likely pathogenic | RCV000035088.2 |
TAZ | rs397515740 | likely pathogenic | RCV000035089.2 |
TAZ | rs397515741 | pathogenic | RCV000035090.2 |
TAZ | rs397515746 | likely pathogenic | RCV000035097.2 |
TAZ | rs397515747 | likely pathogenic | RCV000035098.2 |
TAZ | rs397515750 | likely pathogenic | RCV000035102.2 |
TAZ | rs587776741 | pathogenic | RCV000011861.2 |
TAZ | rs727504327 | likely pathogenic | RCV000154422.1 |
TAZ | rs727504394 | pathogenic | RCV000154564.1 |
TAZ | rs727504431 | likely pathogenic | RCV000154666.1 |