Glycogen storage disease with hypertrophic cardiomyopathy
General Information (adopted from Orphanet):
Synonyms, Signs: |
GSD with hypertrophic cardiomyopathy Glycogenosis with hypertrophic cardiomyopathy |
Number of Symptoms | 0 |
OrphanetNr: | 217572 |
OMIM Id: |
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ICD-10: |
E74.0 |
UMLs: |
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MeSH: |
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MedDRA: |
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Snomed: |
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Prevalence, inheritance and age of onset:
Prevalence: | No data available. |
Inheritance: |
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Age of onset: |
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Disease classification (adopted from Orphanet):
Parent Diseases: |
Rare familial disorder with hypertrophic cardiomyopathy
-Rare cardiac disease -Rare genetic disease |
Comment:
This term does not characterize a disease but a group of diseases. |
Symptom Information:
Associated genes:
ClinVar (via SNiPA)
Gene symbol | Variation | Clinical significance | Reference |
---|---|---|---|
LAMP2 | rs104894857 | pathogenic | RCV000010662.3 |
LAMP2 | rs104894858 | pathogenic | RCV000010663.3 |
LAMP2 | rs104894859 | pathogenic | RCV000010664.4 |
LAMP2 | rs137852527 | pathogenic | RCV000010655.4 |
LAMP2 | rs193922649 | likely pathogenic | RCV000037418.2 |
LAMP2 | rs397516736 | likely pathogenic | RCV000037408.2 |
LAMP2 | rs397516736 | likely pathogenic | RCV000037407.2 |
LAMP2 | rs397516738 | likely pathogenic | RCV000037410.2 |
LAMP2 | rs397516739 | likely pathogenic | RCV000037411.2 |
LAMP2 | rs397516740 | likely pathogenic | RCV000037412.2 |
LAMP2 | rs397516743 | pathogenic | RCV000037416.2 |
LAMP2 | rs397516751 | likely pathogenic | RCV000037432.2 |
LAMP2 | rs397516752 | likely pathogenic | RCV000037433.2 |
LAMP2 | rs727503118 | pathogenic | RCV000150911.1 |
LAMP2 | rs727503119 | pathogenic | RCV000150912.1 |
LAMP2 | rs727503120 | likely pathogenic | RCV000150913.1 |
LAMP2 | rs727504262 | likely pathogenic | RCV000154245.1 |
LAMP2 | rs727504557 | likely pathogenic | RCV000155721.1 |
LAMP2 | rs727504597 | pathogenic | RCV000155777.1 |
LAMP2 | rs727504600 | pathogenic | RCV000155846.1 |
LAMP2 | rs727504648 | pathogenic | RCV000155911.1 |
LAMP2 | rs727504742 | pathogenic | RCV000156041.1 |
LAMP2 | rs730880344 | likely pathogenic | RCV000154670.1 |