Steel syndrome is characterized by characteristic facies, dislocated hips and radial heads, carpal coalition (fusion of carpal bones), short stature, scoliosis, and cervical spine anomalies. The dislocated hips are resistant to surgical intervention (summary by Flynn et al., ... Steel syndrome is characterized by characteristic facies, dislocated hips and radial heads, carpal coalition (fusion of carpal bones), short stature, scoliosis, and cervical spine anomalies. The dislocated hips are resistant to surgical intervention (summary by Flynn et al., 2010).
Steel et al. (1993) reported 23 children from Puerto Rico with dislocated hips and radial heads, carpal coalition (fusion of carpal bones), and short stature. Carpal coalition was identified radiographically and did not interfere with hand or wrist ... Steel et al. (1993) reported 23 children from Puerto Rico with dislocated hips and radial heads, carpal coalition (fusion of carpal bones), and short stature. Carpal coalition was identified radiographically and did not interfere with hand or wrist function. Eight of 23 patients had bilateral talipes cavus, and 3 patients had anomalies of the cervical spine. Flynn et al. (2010) reported 32 patients with this condition, including 18 patients previously reported by Steel et al. (1993). Congenital hip dislocations were present in all patients. Nearly all patients (29/32) had radial head dislocation, and carpal coalition was seen in 73% of wrists. Scoliosis was seen in over half (17/32), and cavus was seen in 34% of feet. All patients had short stature. Most patients had a characteristic facies including long and oval-shaped face, prominent forehead, hypertelorism, and broad nasal bridge.