Reduced number of teeth

Symptom Information:

Symptom ID: HPO:0009804
Cross references:
Is a (Direct Parents):
HPO         Abnormal number of teeth
Is a (Whole tree): HPO:
    Phenotypic abnormality(HPO:0000118)
       Abnormality of head or neck(HPO:0000152)
          Abnormality of the head(HPO:0000234)
             Abnormality of the face(HPO:0000271)
                Abnormality of the mouth(HPO:0000153)
                   Abnormality of the oral cavity(HPO:0000163)
                      Abnormality of the teeth(HPO:0000164)
                         Abnormal number of teeth(HPO:0006483)
                            Reduced number of teeth(HPO:0009804)
Database Frequency: 137 / 7739

All diseases associated with this symptom:

12q14 microdeletion syndrome (Orphanet:94063)
19p13.12 microdeletion syndrome (Orphanet:254346)
2q32q33 microdeletion syndrome (Orphanet:251019)
Acro-oto-ocular syndrome (Orphanet:2980)
Acrofacial dysostosis, Catania type (Orphanet:1786)
Acrofacial dysostosis, Palagonia type (Orphanet:1787)
Acrofacial dysostosis, Weyers type (Orphanet:952)
Amelo-onycho-hypohidrotic syndrome (Orphanet:1028)
Ankyloblepharon - ectodermal defects - cleft lip/palate (Orphanet:1071)
Ankyloblepharon filiforme - imperforate anus (Orphanet:1074)
Anodontia (Orphanet:99797)
Arrhinia - choanal atresia - microphthalmia (Orphanet:1135)
Autosomal dominant Robinow syndrome (Orphanet:3107)
Autosomal dominant hypohidrotic ectodermal dysplasia (Orphanet:1810)
Autosomal dominant microcephaly (Orphanet:2514)
Autosomal recessive Robinow syndrome (Orphanet:1507)
Autosomal recessive hypohidrotic ectodermal dysplasia (Orphanet:248)
Axenfeld-Rieger syndrome (Orphanet:782)
Blepharonasofacial malformation syndrome (Orphanet:1252)
Bloom syndrome (Orphanet:125)
Brachydactyly - mesomelia - intellectual deficit - heart defects (Orphanet:1277)
Branchio-oculo-facial syndrome (Orphanet:1297)
Böök syndrome (Orphanet:1262)
CHARGE syndrome (Orphanet:138)
Cardiomyopathy, dilated, with woolly hair, keratoderma, and toothagenesis (OMIM:615821)
Cenani-Lenz syndrome (Orphanet:3258)
Cerebellar ataxia - ectodermal dysplasia (Orphanet:1174)
Cerebro-oculo-nasal syndrome (Orphanet:66625)
Char syndrome (Orphanet:46627)
Charlie M syndrome (Orphanet:1406)
Cherubism (Orphanet:184)
Cleft lip/palate - deafness - sacral lipoma (Orphanet:2003)
Cleft palate - stapes fixation - oligodontia (Orphanet:2010)
Coffin-Lowry syndrome (Orphanet:192)
Cohen syndrome (Orphanet:193)
Congenital unilateral hypoplasia of depressor anguli oris (Orphanet:1166)
Cornelia de Lange syndrome (Orphanet:199)
Cranioectodermal dysplasia (Orphanet:1515)
Craniofaciofrontodigital syndrome (Orphanet:363705)
Craniolenticulosutural dysplasia (Orphanet:50814)
Craniosynostosis - fibular aplasia (Orphanet:1533)
Cutis gyrata - acanthosis nigricans - craniosynostosis (Orphanet:1555)
Deafness - oligodontia (Orphanet:3230)
Deafness - onychodystrophy (Orphanet:3231)
Deafness with labyrinthine aplasia, microtia, and microdontia (Orphanet:90024)
Dental ankylosis (Orphanet:1077)
Dermatoosteolysis, Kirghizian type (Orphanet:1657)
Dermo-odonto dysplasia (Orphanet:1660)
Distal monosomy 6p (Orphanet:96125)
Dysostosis, Stanescu type (Orphanet:1798)
EEC syndrome (Orphanet:1896)
EEM syndrome (Orphanet:1897)
Ectodermal dysplasia, Berlin type (Orphanet:1816)
Ectodermal dysplasia, tricho-odonto-onychial type (Orphanet:1818)
Ehlers-Danlos syndrome, classic type (Orphanet:287)
Ellis Van Creveld syndrome (Orphanet:289)
Epidermolysis bullosa simplex with anodontia/hypodontia (Orphanet:2325)
Extrasystoles - short stature - hyperpigmentation - microcephaly (Orphanet:1964)
Faciocardiorenal syndrome (Orphanet:1973)
Focal dermal hypoplasia (Orphanet:2092)
Gorlin-Chaudhry-Moss syndrome (Orphanet:2095)
Hennekam syndrome (Orphanet:2136)
Holoprosencephaly (Orphanet:2162)
Hutchinson-Gilford progeria syndrome (Orphanet:740)
Hypodontia - dysplasia of nails (Orphanet:2228)
Hypoglossia - hypodactyly (Orphanet:989)
Hypohidrotic ectodermal dysplasia (Orphanet:238468)
Ichthyosis - hypotrichosis - sclerosing cholangitis (Orphanet:59303)
Incontinentia pigmenti (Orphanet:464)
Intellectual deficit - athetosis - microphthalmia (Orphanet:1236)
Johanson-Blizzard syndrome (Orphanet:2315)
KBG syndrome (Orphanet:2332)
Kabuki syndrome (Orphanet:2322)
Kallmann syndrome (Orphanet:478)
Koolen-De Vries syndrome (Orphanet:96169)
Lacrimo-auriculo-dento-digital syndrome (Orphanet:2363)
Laron syndrome (Orphanet:633)
Lowry-MacLean syndrome (Orphanet:2409)
MEHMO syndrome (Orphanet:85282)
Macrocephaly - short stature - paraplegia (Orphanet:2427)
Maxillo-nasal dysplasia (Orphanet:1248)
Microcephalic osteodysplastic primordial dwarfism type 2 (Orphanet:2637)
Moebius syndrome (Orphanet:570)
Mutilating palmoplantar keratoderma with periorificial keratotic plaques (Orphanet:659)
Non-eruption of teeth - maxillary hypoplasia - genu valgum (Orphanet:2972)
Oculocerebrorenal syndrome (Orphanet:534)
Oculodental syndrome, Rutherfurd type (Orphanet:2709)
Oculodentodigital dysplasia (Orphanet:2710)
Oculofaciocardiodental syndrome (Orphanet:2712)
Oculoosteocutaneous syndrome (Orphanet:2713)
Odonto-onycho dysplasia - alopecia (Orphanet:2722)
Odonto-onycho-dermal dysplasia (Orphanet:2721)
Odontotrichomelic syndrome (Orphanet:2723)
Oligodontia (Orphanet:99798)
Opitz G/BBB syndrome (Orphanet:2745)
Orofaciodigital syndrome type 1 (Orphanet:2750)
Orofaciodigital syndrome type 2 (Orphanet:2751)
Osteodysplasty, Melnick-Needles type (Orphanet:2484)
Osteoglophonic dwarfism (Orphanet:2645)
Otodental syndrome (Orphanet:2791)
Otopalatodigital syndrome (Orphanet:669)
Otopalatodigital syndrome type 1 (Orphanet:90650)
Otopalatodigital syndrome type 2 (Orphanet:90652)
Papillon-Lefèvre syndrome (Orphanet:678)
Pilodental dysplasia - refractive errors (Orphanet:2892)
Postaxial polydactyly - dental and vertebral anomalies (Orphanet:2916)
Progeria - short stature - pigmented nevi (Orphanet:2959)
Progeroid syndrome, Petty type (Orphanet:2963)
Proteus syndrome (Orphanet:744)
Richieri Costa-Pereira syndrome (Orphanet:3102)
Rothmund-Thomson syndrome (Orphanet:2909)
Schöpf-Schulz-Passarge syndrome (Orphanet:50944)
Seckel syndrome (Orphanet:808)
Short stature - wormian bones - dextrocardia (Orphanet:2863)
Smith-Lemli-Opitz syndrome (Orphanet:818)
Smith-Magenis syndrome (Orphanet:819)
Splenogonadal fusion - limb defects - micrognathia (Orphanet:2063)
Stickler syndrome (Orphanet:828)
Stoll-Alembik-Finck syndrome (Orphanet:3200)
Symptomatic form of Coffin-Lowry syndrome in female carriers (Orphanet:276630)
Taurodontia - absent teeth - sparse hair (Orphanet:2731)
Teebi-Shaltout syndrome (Orphanet:3291)
Treacher-Collins syndrome (Orphanet:861)
Tricho-odonto-onychial dysplasia (Orphanet:3355)
Tricho-retino-dento-digital syndrome (Orphanet:1264)
Trichodental syndrome (Orphanet:3351)
Trichodermodysplasia - dental alterations (Orphanet:3353)
Ulnar-mammary syndrome (Orphanet:3138)
Van der Woude syndrome (Orphanet:888)
Ventricular extrasystoles with syncopal episodes - perodactyly - Robin sequence (Orphanet:3201)
W syndrome (Orphanet:2804)
Weaver-Williams syndrome (Orphanet:3448)
Williams syndrome (Orphanet:904)
Wilson-Turner syndrome (Orphanet:3459)
Wolf-Hirschhorn syndrome (Orphanet:280)
Zlotogora-Ogur syndrome (Orphanet:3253)
Zunich-Kaye syndrome (Orphanet:3474)